iNeu™ Human Neural Stem Cells - Friedreich's Ataxia Patient, Donor 45
[CAT#: NRZP-0622-ZP72]
Human iPSC-derived neural stem cells from patients with Friedreich's ataxia
- Species:
- Human
- Applications:
- Cell Culture
- Cell Types:
- Neural Stem Cells
Certificate of Analysis Lookup
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Lot Number
To download a Certificate of Analysis, please enter a lot number in the search box below. Note: Certificate of Analysis not available for kit components.
Lot Number
Product Overview
Description
Friedreich's ataxia (FRDA or FA) is an autosomal recessive disorder caused by mutations in the FXN gene on chromosome 9, which produces a protein called frataxin. Creative Biolabs cell lines from Friedreich's ataxia patients and familial and unaffected controls are excellent models for studying this rare genetic disorder that causes progressive neurological damage and motor problems. Creative Biolabs now offers custom human iPSC-derived sensory neurons or cardiomyocytes derived from Friedreich's ataxia patients.
Cell Types
Neural Stem Cells
Applications
Cell Culture
Relevant Diseases
Ataxia
Species
Human
Properties
Tissue Source
Fibroblasts
Shipping
Dry ice
Storage
Liquid Nitrogen Vapor Phase
Research Use Only
For research use only. They are not approved for human or animal use, or for application in in vitro diagnostic procedures.
Donor Information
Gender
Female
Donor Age
17
Donor Health
Disease
Additional Donor Information
Gene Type: FXN
Publications
Publications (0)
Neural Cell Lines
For Research Use Only. Not For Clinical Use.
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